Histopathologic abnormalities of the lymphoreticular tissues in organic cation transporter 2 deficiency: evidence for impaired B cell maturation.

Komlósi, Katalin; Havasi, Viktória; Bene, Judit; Süle, Norbert; Pajor, László; Nicolai, Raffaella; Benatti, Paola; Calvani, Menotti et al. · J Pediatr · 2007

case_report · Level V

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Abstract

Immunohistology of lymphoreticular tissues of a fatal case of organic cation transporter 2 deficiency revealed inhibited proliferation with increased apoptosis in the germinal centers, resulting in "burned out" follicles. This is indicative of impaired antigen driven B cell affinity maturation. Defective humoral immune response might explain the recurrent infections in untreated organic cation transporter 2 deficiency.

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