Cognitive prognosis of patients with tuberous sclerosis complex.

Winterkorn, Elisabeth B; Pulsifer, Margaret B; Thiele, Elizabeth A · Neurology · 2007

retrospective_cohort · Level III

Where this comes from

Abstract

To assess cognitive outcome in patients with tuberous sclerosis complex (TSC) and identify predictive risk factors, we reviewed records of 107 patients who underwent comprehensive neuropsychiatric evaluation. Fifty-seven percent of patients with TSC had normal-range IQ/developmental quotient (DQ). Cognitive outcome was strongly associated with refractory seizures and TSC2 mutation. In TSC, IQ/DQ is bimodally distributed, and more than half of individuals are in the normal range.

Medical subject headings