One-step surgical approach of a thoracic aortic aneurysm in Wiskott-Aldrich syndrome.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 17383380.
- No licence information is recorded for this record.
- Because redistribution is not established, this page shows the abstract only. Follow the links below for the full text.
Abstract
Wiskott-Aldrich syndrome is a primary immunodeficiency characterized by infections, thrombocytopenia, and eczema. We present a 33-year-old man with this syndrome who underwent a one-stage ascending aorta, aortic arch and descending aortic aneurysm repair under moderate hypothermia and continuous visceral and cerebral perfusion. Histologic examination showed the presence of an aortitis with granulomatous inflammatory response and multinucleated cells.
Medical subject headings
- Aortic Aneurysm, Thoracic
- Blood Vessel Prosthesis Implantation
- Wiskott-Aldrich Syndrome