Aplasia of the right aortic cusp in a neonate: a life-threatening but curable anomaly.

Henze, A C; Malm, T K; Sunnegårdh, J T; Hallberg, M B · Ann Thorac Surg · 1991

case_report · Level V

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Abstract

A case of absent right aortic cusp causing serious aortic incompetence in a neonate is reported. A "bicuspidalization" repair broke down within 24 hours, but reoperation with annular enlargement and insertion of a 19-mm prosthetic valve resulted in complete recovery. This rare but life-threatening anomaly of the aortic valve can be recognized with Doppler echocardiography. Valve replacement in conjunction with aortic annular enlargement should be performed as primary repair.

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