Mitochondrial DNA sequence analysis in congenital myotonic dystrophy.

Thyagarajan, D; Byrne, E; Noer, S; Lertrit, P; Utthanophol, P; Kapsa, R; Marzuki, S · Ann Neurol · 1991

case_series · Level IV

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Abstract

Mitochondrial genetic modifying factors have been suspected in several autosomally inherited diseases. The congenital variant of myotonic dystrophy, in which there is striking maternal inheritance pattern, is a likely candidate disease. To investigate this possibility, we sequenced completely the mitochondrial genome in 2 patients with congenital myotonic dystrophy. Comparison of the two sequences with control data failed to reveal a specific nucleotide variant or length variant in this disease. We conclude that a mitochondrial genetic modifying factor is not present in congenital myotonic dystrophy.

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