Diffuse pulmonary angiomatosis.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 1771607.
- Also identified by PMC identifier 1021043.
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Abstract
A six year old girl with diffuse pulmonary angiomatosis presented with haemoptysis and diffuse interstitial changes with bilateral pleural effusions on the chest radiograph. The lung lesion as seen on biopsy specimens (and confirmed at necropsy) consisted of bloodless, thin walled, endothelium lined channels, affecting the interstitial septae, pleura, bronchi, and adventitia of large vessels. There was no response to oral corticosteroids or a trial of cyclosphamide. This lesion may be an example of an angiogenic disease.
Medical subject headings
- Angiomatosis
- Lung
- Lung Neoplasms