Segmental neurofibromatosis of the hand and upper extremity: a case report.

Ilyas, Asif M; Nourissat, Geoffroy; Jupiter, Jesse B · J Hand Surg Am · 2007

case_report · Level V

Where this comes from

Abstract

A case of segmental neurofibromatosis of the upper extremity is presented. Multiple neurofibromas involving different peripheral nerves limited to a single body part or limb is a rare form of neurofibromatosis. The clinical, genetic, and histologic findings of segmental neurofibromatosis are described. The criteria for segmental neurofibromatosis are reviewed, and the differentiation of neurofibromatosis types 1 and 2 and schwannomatosis is also briefly reviewed.

Medical subject headings

Anatomy