A hypoplastic atlas and long odontoid process in a girl manifesting phenotypic features resembling spondyloepimetaphyseal dysplasia joint laxity syndrome.

Al Kaissi, Ali; Chehida, Farid Ben; Ghachem, Maher Ben; Klaushofer, Klaus; Grill, Franz · Skeletal Radiol · 2008

case_report · Level V

Where this comes from

Abstract

Phenotypic features consistent but not completely diagnostic for spondyloepimetaphyseal dysplasia joint laxity (SEMDJL) were encountered in a 7-year-old-girl. Additional tomographic features of a hypoplastic atlas (assimilation of the posterior arch of the atlas) and unduly long odontoid process were seen. We report what might be a novel type of SEMDJL.

Medical subject headings

Anatomy