Prolonged remission of severe Cushing syndrome without adrenalectomy in an infant with McCune-Albright syndrome.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 18492536.
- Also identified by DOI 10.1016/j.jpeds.2008.01.037.
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Abstract
A 4 month-old girl presented with severe Cushing syndrome caused by McCune-Albright syndrome. After undergoing 19 months of pharmacologic suppression of cortisol production, she has been in clinical remission for more than 6 years. Adrenalectomy may be avoidable even in severe cases of Cushing syndrome associated with McCune-Albright syndrome.
Medical subject headings
- Adrenergic Agents
- Aminoglutethimide
- Cushing Syndrome
- Enzyme Inhibitors
- Fibrous Dysplasia, Polyostotic
- Metyrapone