Vascular malformations as underlying cause of chronic thromboembolism and pulmonary hypertension.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 18571489.
- Also identified by DOI 10.1016/j.bjps.2007.12.062.
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Abstract
We report four patients with chronic thromboembolic pulmonary hypertension (CTEPH) presumably due to recurrent pulmonary embolism from low-flow vascular malformations, and give a review of the literature. Venous malformations, such as those observed in Klippel- Trenaunay syndrome (KTS) can be associated with hypercoagulability, thrombosis and recurrent pulmonary embolism and ultimately CTEPH. Since many physicians appear unfamiliar with these potential complications, patients may experience a delayed diagnosis of this progressive and potentially life-threatening CTEPH.
Medical subject headings
- Hypertension, Pulmonary
- Thromboembolism
- Vascular Malformations