Inflammatory pseudotumor of the choroid plexus in Sjögren's disease.

Chang, Y; Horoupian, D S; Lane, B; Fross, R D; Smyth, L T; Seiling, R J · Neurosurgery · 1991

case_report · Level V

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Abstract

We report an unusual case of inflammatory pseudotumor of the choroid plexus of the right lateral ventricle, manifesting as an intraventricular mass and causing unilateral hydrocephalus in a 48-year-old man who suffered from Sjögren's disease and subacute cutaneous lupus erythematosus. The lesion obliterated the normal choroidal architecture by a mixed chronic inflammatory process that was associated with reactive connective tissue changes. Immunohistochemical studies showed no light-chain restriction in the cells, and residual islands of transthyretin-positive epithelial cells were identified, implicating the choroid plexus origin of the mass.

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