Endoscopic transnasal decompression for management of basilar invagination in osteogenesis imperfecta.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 18939921.
- Also identified by DOI 10.3171/SPI.2008.9.10.354.
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Abstract
Osteogenesis imperfecta (OI) is a disorder of bone development caused by a genetic dysfunction of collagen synthesis. Basilar invagination (BI) is an uncommon but serious complication of OI. Brainstem decompression in OI is undertaken in certain circumstances. Transoral-transpalatopharyngeal ventral decompression with posterior occipitocervical fusion has become the treatment of choice when required. This technical note outlines a novel endoscopic transnasal approach for ventral decompression. The literature is reviewed and a strategy for the management of BI in patients with OI is outlined.
Medical subject headings
- Decompression, Surgical
- Endoscopy
- Osteogenesis Imperfecta
- Platybasia