Acquired cutis laxa associated with heavy chain deposition disease.

Harrington, Cynthia R; Beswick, Tracy C; Susa, Joseph S; Pandya, Amit G · J Am Acad Dermatol · 2008

case_report · Level V

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Abstract

Acquired cutis laxa (generalized acquired elastolysis) is a condition of unknown etiology characterized by a degeneration of elastic fibers in the skin, resulting in laxity with reduced elastic recoil. We describe a patient with acquired cutis laxa associated with an underlying heavy chain deposition disease. Direct immunofluorescence testing of lesional skin demonstrated immunoglobulin G deposition on elastic fibers, suggesting that in some cases, cutis laxa may have an immune-mediated etiopathogenesis.

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