Camurati-Engelmann disease: imaging, clinical features and differential diagnosis.

Bartuseviciene, Aldona; Samuilis, Arturas; Skucas, Jovitas · Skeletal Radiol · 2009

case_series · Level IV

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Abstract

We report four sporadic and three familial patients with Camurati-Engelmann disease. One patient had follow-up examinations over 8 years. Pain in the extremities and muscle weakness were common clinical symptoms. Most patients also had cranial nerve impairment, hepatosplenomegaly, a waddling gait, and elevated serum alkaline phosphatase levels. Long bones were affected in all. We discuss the differential diagnosis for this interesting bone entity.

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