Prion topology and toxicity.

Aguzzi, Adriano; Steele, Andrew D · Cell · 2009

basic_science · Level V

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Abstract

Inactivation of mahogunin, an E3 ubiquitin ligase, causes a spongiform encephalopathy resembling prion disease. Chakrabarti and Hegde (2009) now report that prion proteins with aberrant topologies inactivate mahogunin, providing a plausible explanation for certain aspects of prion pathology.

Medical subject headings