Successful surgical pulmonary artery reconstruction in arterial tortuosity syndrome.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 19766840.
- Also identified by DOI 10.1016/j.athoracsur.2009.02.020.
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Abstract
The outcomes of surgical repair for diffuse pulmonary artery stenoses due to arterial tortuosity syndrome are unknown. We report a 1-year-old girl with tortuosity syndrome who presented with suprasystemic right ventricular pressure due to distortion and stenoses of the pulmonary artery branches. We describe the operative findings of this unique pathology and the surgical techniques used to completely reconstruct the pulmonary arterial tree, with normalization of the right ventricular pressure.
Medical subject headings
- Arterial Occlusive Diseases
- Pulmonary Artery
- Stents
- Vascular Malformations
- Vascular Surgical Procedures