Primary pulmonary rhabdomyosarcoma in an adult with neurofibromatosis-1.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 19766846.
- Also identified by DOI 10.1016/j.athoracsur.2009.02.083.
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Abstract
Rhabdomyosarcomas arising in various tissues associated with neurofibromatosis type 1 have been sporadically described in children and young adults. We report a unique case of primary pulmonary rhabdomyosarcoma in an adult with neurofibromatosis type 1. A right lower lobectomy was performed. The Intergroup Rhabdomyosarcoma Study IV postsurgical grouping classification was 1A. The patient is scheduled for chemotherapy without adjuvant radiation therapy as per standard pediatric protocol.
Medical subject headings
- Lung Neoplasms
- Neurofibromatosis 1
- Rhabdomyosarcoma