Rosai-Dorfman disease presenting as a pulmonary artery mass.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 20103266.
- Also identified by DOI 10.1016/j.athoracsur.2009.05.016.
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Abstract
Rosai-Dorfman disease is rare and typically presents with cervical lymphadenopathy, but may manifest as extranodal disease. This disease is generally indolent and self-limited, but it carries a poor or fatal prognosis when it is advanced or when it involves and compresses vital structures. We present a case of Rosai-Dorfman disease affecting the pulmonary arteries in a 22-year-old woman with severe, symptomatic right heart failure.
Medical subject headings
- Histiocytosis, Sinus
- Pulmonary Artery
- Vascular Diseases
- Vascular Surgical Procedures