Orthopaedic manifestations of Rett syndrome.

Guidera, K J; Borrelli, J; Raney, E; Thompson-Rangel, T; Ogden, J A · J Pediatr Orthop · 1991

case_series · Level IV

Where this comes from

Abstract

We reviewed nine patients with Rett syndrome, a progressive encephalopathy that is being diagnosed more frequently in the United States. It occurs in females, causing mental deterioration, autistic behavior, and classic hand-wringing motion. The orthopaedic manifestations include scoliosis, lower extremity contracture, and coxa valga. Bracing and surgery are indicated to prevent or correct deformity and maintain ambulation.

Medical subject headings

Anatomy