Fatty infiltration in the liver in medium chain acyl CoA dehydrogenase deficiency.

Losty, H C; Lee, P; Alfaham, M; Gray, O P; Leonard, J V · Arch Dis Child · 1991

case_report · Level V

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Abstract

Fatty infiltration of the liver at postmortem examination has been recommended as a criterion for selection of infants who have died suddenly and unexpectedly for further biochemical investigation for disorders of fatty acid oxidation. We describe a boy with medium chain acyl CoA dehydrogenase deficiency who died four months after diagnosis and in whom only minimal hepatic fatty infiltration was found.

Medical subject headings