Successful treatment of adult Henoch-Schönlein purpura with factor XIII concentrate.

Utani, A; Ohta, M; Shinya, A; Ohno, S; Takakuwa, H; Yamamoto, T; Suzaki, T; Danno, K · J Am Acad Dermatol · 1991

case_report · Level V

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Abstract

We report the cases of three adult patients with severe abdominal complications of Henoch-Schönlein purpura who had low activity of factor XIII during the acute phase of the disease. In all three cases, abdominal symptoms and purpura immediately responded to heat-treated, placenta-derived factor XIII concentrate. No adverse effects were experienced. Factor XIII concentrate replacement should be considered as the initial treatment for severe abdominal symptoms in adult Henoch-Schönlein purpura associated with a decreased level of factor XIII activity.

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