Circumflex right aortic arch with associated hypoplasia and coarctation: repair by aortic arch advancement and end-to-side anastomosis.

Abstract

Right aortic arch with associated arch hypoplasia, coarctation, and an aberrant isolated left subclavian artery is a very uncommon variant of vascular rings, which itself accounts for fewer than 1% of all congenital cardiac defects. Several cases have been reported, and most commonly, extraanatomic grafts have been used for repair. We present a unique technique that involves the resection of the circumflex arch, aortic arch advancement, and end-to-side anastomosis to repair this rare aortic arch malformation.