Interleukin-12 receptor β1 deficiency predisposing to disseminated Coccidioidomycosis.

Vinh, Donald C; Schwartz, Brian; Hsu, Amy P; Miranda, David J; Valdez, Patricia A; Fink, Danielle; Lau, Karen P; Long-Priel, Debra et al. · Clin Infect Dis · 2011

case_report · Level V

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Abstract

Severe disseminated <i>Coccidioides</i> is rare while localized, contained disease is common. We report a family with disseminated coccidioidomycosis due to a novel homozygous C186Y mutation in interleukin (IL)-12 receptor β1. This family confirms the centrality of the IL-12/IFN-γ axis to human immunity to <i>Coccidioides</i> spp.

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