Immunoglobulin G4-related periaortitis mimicking an intramural hematoma.

Byeon, Kyeongmin; Han, Joungho; Kim, Jung-Sun; Kim, Wook Sung; Choe, Yeon Hyeon; Lee, Eun Jeong; Kim, Duk-Kyung · Ann Thorac Surg · 2011

case_report · Level V

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Abstract

Immunoglobulin G4 (IgG4)-related sclerosing disease in the cardiovascular system is a recently proposed disease entity, which is still unfamiliar to most clinicians. We present a case of IgG4-related periaortitis of the ascending aorta mimicking an intramural hematoma in the computed tomography (CT) scan, which led to an unnecessary surgery. IgG4-related periaortitis needs to be considered in the differential diagnosis in a patient with thickened aortic wall because the disease should be treated medically in light of its good response to steroid therapy.

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