Skin manifestations in congenital deficiency of leucocyte-adherence glycoproteins (CDLG).
case_report · Level V
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- Record sourced from PubMed, PMID 2206977.
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Abstract
In congenital deficiency of leucocyte-adherence glycoproteins (CDLG) there is an immunodeficiency with impaired leucocyte function and cutaneous and extracutaneous infections occur. In more than 30% of cases the condition has a fatal course. We report the skin manifestations of three siblings with CDLG in which areas of skin necrosis occurred that resembled pyoderma gangrenosum.
Medical subject headings
- Leukocyte-Adhesion Deficiency Syndrome
- Metabolism, Inborn Errors
- Skin Ulcer