Pulmonary tumor thrombotic microangiopathy with cor pulmonale due to desmoplastic small round cell tumor.

Sadimin, Evita T; Collier, Adrienne G; Gaffney, Joseph W; Fyfe, Billie · J Pediatr · 2012

case_report · Level V

Where this comes from

Abstract

A 12-year-old boy presented acutely after an episode of syncope with perioral cyanosis. He died 19 hours after admission due to cor pulmonale as a complication of metastatic desmoplastic small round cell tumor in the lungs with associated tumor thrombotic microangiopathy.

Medical subject headings