Maffucci's syndrome with bilateral cartilaginous tumors of the cerebellopontine angle.
case_report · Level V
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Abstract
Maffucci's syndrome is characterized by the combination of multiple enchondromas (Ollier's disease) and hemangiomatosis. These hemangiomas develop in the subcutaneous tissue and form red-blue tumors dispersed over the whole body. Intracranial involvement is rare, making a preoperative radiological diagnosis and differentiation from other tumors rather difficult. The radiological characteristics and successful removal of the intracranial part of a chondrosarcoma of the cerebellopontine angle in a case of Maffucci's syndrome are reported in this paper.
Medical subject headings
- Chondrosarcoma
- Enchondromatosis
- Skull Neoplasms