Severe cyanosis after Kawashima operation resulting from congenital portosystemic shunt.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 22450089.
- Also identified by DOI 10.1016/j.athoracsur.2011.08.058.
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Abstract
We describe an unusual case of a patient with polysplenia, inferior vena cava (IVC) interruption, and unrecognized congenital portosystemic venous connection (CPVC) in whom severe cyanosis developed in the acute postoperative stage after a Kawashima operation and required urgent surgical division of the CPVC. It has been stressed recently that CPVCs and other abdominal venous abnormalities have been underdiagnosed in patients with polysplenia and IVC interruption, and we think that a routine evaluation of abdominal venous connections should be mandatory before considering the Kawashima operation for these patients.
Medical subject headings
- Cyanosis
- Heterotaxy Syndrome
- Vascular Malformations
- Vascular Surgical Procedures
- Veins
- Vena Cava, Inferior