Branchi-oculo-facial syndrome: a case report to highlight recent genetic considerations.

Abbo, Olivier; Bieth, Eric; Ballouhey, Quentin; Vaysse, Frederic; Just, Walter; Galinier, Philippe · J Plast Reconstr Aesthet Surg · 2012

case_report · Level V

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Abstract

Branchio-oculo-facial syndrome (BOFS) is a rare entity described during the last century which has been recently linked to mutations of the gene encoding for the transcription factor named 'TFAPA2'. We report here a sporadic case of BOFS with a partial phenotype caused by a de novo mutation of this gene and discuss recent genetic findings.

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