Stiff-man syndrome: a GABAergic autoimmune disorder with autoantigenic heterogeneity.

Gorin, F; Baldwin, B; Tait, R; Pathak, R; Seyal, M; Mugnaini, E · Ann Neurol · 1990

case_report · Level V

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Abstract

Autoantibodies that reacted with cell bodies and axon terminals of gamma-aminobutyric acid (GABA)ergic neurons were present in the serum and cerebrospinal fluid in a patient with stiff-man syndrome with type I diabetes. Immunoblot experiments using this patient's serum and cerebrospinal fluid did not corroborate an earlier observation that these autoantibodies are directed against the GABAergic cytosolic enzyme, L-glutamic acid decarboxylase. While L-glutamic acid decarboxylase autoantibodies may be associated with this syndrome, they do not appear to be easily demonstrated.

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