Pulmonary extranodal marginal zone lymphoma of mucosa-associated lymphoid tissue associated with granulomatous inflammation in a child with chromosome 22q11.2 deletion syndrome (DiGeorge syndrome).
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 22920507.
- Also identified by DOI 10.1016/j.jpeds.2012.07.003 and PMC identifier 3700545.
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Abstract
Patients with immunodeficiency disorders have an increased incidence of lymphoproliferative disorders; however, only 4 such patients with DiGeorge/chromosome 22q11.2 deletion syndrome have been reported. We report a case of a pulmonary Epstein-Barr virus-negative extranodal marginal zone lymphoma of mucosa-associated lymphoid tissue in a child with this syndrome.
Medical subject headings
- DiGeorge Syndrome
- Gene Deletion
- Inflammation
- Lymphoma, B-Cell, Marginal Zone