IgG4-related systemic disease presenting with lung entrapment and constrictive pericarditis.
case_report · Level V
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- Record sourced from PubMed, PMID 22948582.
- Also identified by DOI 10.1378/chest.11-2608.
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Abstract
We describe a 29-year-old woman who presented with chronic pleuropericarditis complicated by lung entrapment and constrictive pericarditis. Pleural biopsy performed during the decortication procedure revealed fibrinous pleuritis with lymphoplasmacytic inflammation including IgG4-positive plasma cells. The patient responded favorably to corticosteroid therapy with resolution of pleural effusion and constrictive physiology. To our knowledge, this is the first reported case of IgG4-related systemic disease manifesting as lung entrapment and constrictive pericarditis.
Medical subject headings
- Immunoglobulin G
- Pericarditis
- Pericarditis, Constrictive
- Pleurisy