Imatinib mesylate in the treatment of diffuse cutaneous mastocytosis.

Morren, Marie-Anne; Hoppé, Anne; Renard, Marleen; Debiec Rychter, Maria; Uyttebroeck, Anne; Dubreuil, Patrice; Martin, Ludovic · J Pediatr · 2013

case_report · Level V

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Abstract

Diffuse cutaneous mastocytosis is a less common but potentially life-threatening variant of childhood mastocytosis. Here we report 2 children with diffuse cutaneous mastocytosis in whom an activating somatic KIT mutation was detected. Treatment with imatinib, a KIT inhibitor, resulted in resolution of the lesions and were well tolerated by the patients.

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