Common variable immunodeficiency as the initial presentation of dyskeratosis congenita.

Allenspach, Eric J; Bellodi, Cristian; Jeong, David; Kopmar, Noam; Nakamura, Tomoka; Ochs, Hans D; Ruggero, Davide; Skoda-Smith, Suzanne et al. · J Allergy Clin Immunol · 2013

case_report · Level V

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Abstract

We present a case highlighting the clinical overlap between Common Variable Immunodeficiency (CVID) and Dyskeratosis Congenita (DC). It demonstrates that DC may initially present as an isolated humoral immunodeficiency resembling CVID.

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