Propofol-related infusion syndrome heralding a mitochondrial disease: case report.

Savard, Martin; Dupré, Nicolas; Turgeon, Alexis F; Desbiens, Richard; Langevin, Stephan; Brunet, Denis · Neurology · 2013

case_report · Level V

Where this comes from

Abstract

Propofol-related infusion syndrome (PRIS) is a rare but catastrophic complication of propofol use. It is clinically characterized by metabolic acidosis, rhabdomyolysis, arrhythmias, myocardial failure, renal failure, and hepatomegaly, and may lead to death.<sup>1</sup> Some risk factors are associated with PRIS, namely young age, critical illness, high fat intake, catecholamine or steroid use, inborn error of fatty acid oxidation, propofol doses exceeding 4–5 mg/kg/hour, and duration of use exceeding 48 hours.<sup>1</sup> Some evidence also suggests that PRIS is related to a mitochondrial toxicity of propofol.<sup>2,3</sup>

Medical subject headings