Loeys-Dietz syndrome with bilateral radial head dislocations: a case report.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 24014798.
- No licence information is recorded for this record.
- Because redistribution is not established, this page shows the abstract only. Follow the links below for the full text.
Abstract
Loeys-Dietz syndrome is characterised by vascular aneurysms, hypertelorism, and a bifid uvula. We report on an 11-year-old boy with Loeys-Dietz syndrome who presented with bilateral radial head dislocations and severe osteopaenia with changes of avascular necrosis in both hips causing an out-toeing, wide gait. Considering the poor prognosis for elbow movement and possible radial head dysplasia, surgical reduction of the radial heads was deferred. A subtrochanteric de-rotation osteotomy of the left hip was performed to improve the gait.
Medical subject headings
- Bone Diseases, Metabolic
- Femur Head Necrosis
- Joint Dislocations
- Loeys-Dietz Syndrome
- Wrist Joint
Anatomy
- radius
- femur
- wrist