Treatment of congenital generalized lymphangiectasia with propranolol in a preterm infant.

Poralla, Christine; Specht, Sabine; Born, Mark; Müller, Annette; Bartmann, Peter; Müller, Andreas · Pediatrics · 2014

case_report · Level V

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Abstract

Generalized lymphangiectasia is a rare congenital disorder characterized by dilated lymphatic vessels with a fatal prognosis, especially in cases with thoracic involvement. We describe the use of propranolol in the therapy of generalized lymphangiectasia in a preterm infant with hydrops fetalis. Propranolol was well tolerated and effective within the first months. It remains to be shown whether propranolol is a treatment option for infants with generalized lymphangiectasia.

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