Gain-of-function signal transducer and activator of transcription 1 (STAT1) mutation-related primary immunodeficiency is associated with disseminated mucormycosis.

Kumar, Nilay; Hanks, Mary E; Chandrasekaran, Prabha; Davis, Brian C; Hsu, Amy P; Van Wagoner, Nicholas J; Merlin, Jessica S; Spalding, Christine et al. · J Allergy Clin Immunol · 2014

case_report · Level V

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Abstract

We identified a novel gain of function mutation in <i>STAT1</i> in a patient with disseminated <i>Apophysomyces trapeziformis</i> infection who had never had mucocutaneous candidiasis or autoimmunity. To our knowledge this is the first report of a genetic predisposition associated with mucormycosis.

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