Antecollis and levodopa-responsive parkinsonism are late features of Dravet syndrome.

Fasano, Alfonso; Borlot, Felippe; Lang, Anthony E; Andrade, Danielle M · Neurology · 2014

case_report · Level V

Where this comes from

Abstract

Dravet syndrome (DS) is a severe genetic epileptic encephalopathy mainly caused by <i>SCN1A</i> mutations.<sup>1</sup> Children usually develop frequent and pharmacoresistant seizures of several types. Besides cognitive delay, some patients later develop gait ataxia. “Crouch gait” has also been described in older patients.<sup>2,3</sup>

Medical subject headings