A woman with warts, leg swelling, and deafness.

Muszynski, Melissa A; Zerbe, Christa S; Holland, Steven M; Kong, Heidi H · J Am Acad Dermatol · 2014

case_report · Level V

Where this comes from

Abstract

KEY TEACHING POINTS • We describe a 45-year-old woman with GATA2 deficiency associated with verrucae, lymphedema, immunodeficiency, and a history of infections and skin cancer. • GATA2 deficiency has variable clinical expressivity with differing presentations, including infection, hematopoietic abnormalities, immunodeficiency, lymphedema, and cancer. • Cutaneous manifestations include verruca vulgaris, soft tissue infections, lymphedema, and panniculitis. • Patients may have verrucae that can progress to squamous cell carcinomas; dermatologists therefore play an important role in managing these patients as members of a multidisciplinary team.

Medical subject headings