Malignant melanoma masquerading as an angiofibroma in a patient with MEN-1.

Brown, G Thomas; Cowen, Edward W; Lee, Chyi-Chia Richard · JAMA Dermatol · 2015

case_report · Level V

Where this comes from

Abstract

Multiple endocrine neoplasia type 1 (MEN-1) is an autosomal dominant syndrome consisting of endocrine tumors of the parathyroid gland, pituitary gland, and pancreas. MEN-1 is caused by loss of function mutations in the <i>MEN1</i> gene, which encodes the tumor suppressor protein menin. Cutaneous collagenomas and facial angiofibromas also have been associated with MEN-1 and may serve as diagnostic clues to the diagnosis. We present a case of amelanotic melanoma resembling a large angiofibroma in a young man with MEN-1.

Medical subject headings