Moyamoya syndrome associated with Alagille syndrome: outcome after surgical revascularization.
case_series · Level IV
Where this comes from
- Record sourced from PubMed, PMID 25465847.
- Also identified by DOI 10.1016/j.jpeds.2014.10.067.
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Abstract
Vasculopathy is well-described in Alagille syndrome (ALGS); however, few data exist regarding neurosurgical interventions. We report 5 children with ALGS with moyamoya who underwent revascularization surgery. Postsurgical complications included 1 stroke and 1 death from thalamic hemorrhage. Global function improved in survivors. Revascularization is reasonably safe in patients with ALGS and may improve neurologic outcomes.
Medical subject headings
- Alagille Syndrome
- Cerebral Revascularization
- Moyamoya Disease