Aorto-Tracheopexy in the Treatment of Hunter Syndrome.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 26046872.
- Also identified by DOI 10.1016/j.athoracsur.2014.08.048.
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Abstract
Hunter syndrome is a multisystem genetic disease in which a significant proportion of morbidity and mortality arise from respiratory dysfunction. Notably, tracheal abnormalities in Hunter syndrome can compromise clinical stability, and management is primarily supportive. We describe here the first successful implementation of aorto-tracheopexy in a 19-year-old patient as a surgical strategy to resolve progressive respiratory deterioration.
Medical subject headings
- Aorta, Thoracic
- Mucopolysaccharidosis II
- Plastic Surgery Procedures
- Sternotomy
- Trachea
- Vascular Surgical Procedures