Merkel cell carcinoma in a patient with GATA2 deficiency: a novel association with primary immunodeficiency.

Crall, C; Morley, K W; Rabinowits, G; Schmidt, B; Dioun Broyles, A; Huang, J T · Br J Dermatol · 2016

case_report · Level V

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Abstract

A 55-year-old woman with GATA2 deficiency and neurofibromatosis 1 was diagnosed with Merkel cell carcinoma (MCC). This polyomavirus-associated cutaneous malignancy has previously been associated with immunosuppression and acquired immunodeficiencies such as HIV/AIDS. However, MCC has not been previously reported in the setting of underlying primary or inherited immunodeficiency.

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