Congenital Absence of One Pulmonary Valve Cusp With Other Hypoplastic Cusps.

Yamazaki, Sachiko; Yamagishi, Masaaki; Nishida, Kouichi; Tamura, Satoshi; Monta, Osamu; Numata, Satoshi; Tsutsumi, Yasushi; Ohashi, Hirokazu · Ann Thorac Surg · 2015

case_report · Level V

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Abstract

Congenital absence of a single pulmonary valve cusp is extremely rare. We report a case of a 38-year-old woman with a confirmed congenital absence of a single pulmonary valve cusp associated with dextrocardia. The other 2 leaflets were moderately hypoplastic, and transthoracic echocardiography showed severe pulmonary regurgitation. This combination of lesions has not been reported previously. Pulmonary valve replacement using a composite biologic valved conduit was performed with an excellent outcome.

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