Males with Paternally Inherited MKRN3 Mutations May Be Asymptomatic.

Dimitrova-Mladenova, Mihaela S; Stefanova, Elisaveta M; Glushkova, Maria; Todorova, Albena P; Todorov, Tihomir; Konstantinova, Maia M; Kazakova, Krasimira; Tincheva, Radka S · J Pediatr · 2016

case_series · Level IV

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Abstract

Ten girls with sporadic central precocious puberty were screened for mutations in the maternally imprinted gene MKRN3. We detected 1 novel frameshift mutation (p.Arg351Serfs*44) and a previously described mutation (p.Pro161Argfs*10). In the course of investigating the family, genetic analysis found 2 asymptomatic males with paternally inherited MKRN3 mutations, which has not been reported in previous studies.

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