Diffuse Alveolar Septal Amyloidosis With Wild-Type Transthyretin With Spontaneous Lung Hematoma.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 30009808.
- Also identified by DOI 10.1016/j.athoracsur.2018.05.096.
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Abstract
We experienced a mass formation in the right lower lobe in a patient with cardiac amyloidosis and heart failure. Radiologic findings of the chest showed no abnormality except a mass. The patient had non-valvular atrial fibrillation and was taking edoxaban. Surgical resection of the mass revealed a hematoma. Further pathologic evaluation revealed diffuse alveolar septal amyloidosis with transthyretin (ATTR). The genetic testing found no mutation in the TTR gene. Therefore, systemic wild-type TTR amyloidosis (ATTRwt) was confirmed. Alveolar septal ATTRwt is rare and patient had alveolar septal ATTRwt with spontaneous lung hematoma.
Medical subject headings
- Amyloid Neuropathies, Familial
- Hematoma
- Lung Diseases
- Pulmonary Alveoli