Isolated Congenital Dysgenesia of a Pulmonary Valve Cusp Presenting as a Pulmonary Artery Aneurysm.

Saedi, Sedigheh; Rezaei-Kalantari, Kiara; Parsaee, Mozhgan; Behjati, Mohaddeseh; Hosseini, Saeid · Ann Thorac Surg · 2019

case_report · Level V

Where this comes from

Abstract

Pulmonary artery aneurysm is a rare disorder, with the underlying pathology remaining obscure in many instances. More common causes include pulmonary hypertension, poststenotic dilation, or vasculitis. In this case series, we report 3 patients presenting with isolated pulmonary artery aneurysms in whom multimodality imaging revealed the dysgenesia of a single pulmonary valve cusp as the cause of the huge pulmonary aneurysm.

Medical subject headings