Immunoglobulin G4 Inflammatory Aortic Aneurysm Mimicking Acute Aortic Syndrome.

Blazekovic, Robert; Planinc, Mislav; Catic, Jasmina; Baric, Davor; Unic, Daniel; Manojlovic, Luka; Holzer, Sabrina · Ann Thorac Surg · 2019

case_report · Level V

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Abstract

Immunoglobulin-G4-related disease (IgG4RD) is a novel clinical entity characterized by lymphoplasmacytic infiltrates presenting as an excessive fibrosis such as retroperitoneal inflammatory pseudotumor but rarely affecting the heart or the aorta. We describe a case of IgG4RD with multifocal aortic involvement presenting as an acute aortic syndrome.

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