Histopathologic and Genetic Features of Alveolar Capillary Dysplasia with Atypical Late Presentation and Prolonged Survival.
case_report · Level V
Where this comes from
- Record sourced from PubMed, PMID 30853201.
- Also identified by DOI 10.1016/j.jpeds.2019.01.047 and PMC identifier 6592752.
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Abstract
Alveolar capillary dysplasia typically presents with neonatal pulmonary hypertension and early mortality. However, there is growing evidence for a subset of disease with atypical late onset and/or prolonged survival. Here, we present the variable clinical, genetic, and pathology findings of 4 such patients.
Medical subject headings
- Lung
- Persistent Fetal Circulation Syndrome
- Pulmonary Alveoli